Dermatofibrosarcoma Protuberans on the Lateral Aspect of Neck: A Rare Case Report

Dermatofibrosarcoma Protuberans (DFSP) is a rare, low-grade, locally aggressive cutaneous soft-tissue tumour with a high propensity for local recurrence and low metastatic potential. It commonly arises over the trunk and extremities, while involvement of the head and neck region is uncommon. Hereby, the authors present a case of a 66-year-old male who presented with a progressively enlarging, painless swelling over the left lateral aspect of the neck for 3-4 months. Clinical examination revealed a well-defined, firm, non tender mass in the subcutaneous plane. Radiological evaluation suggested a cystic nerve sheath tumour. The lesion was excised, and histopathological examination demonstrated a spindle cell tumour arranged in a storiform pattern, consistent with DFSP. The patient subsequently underwent Wide Local Excision (WLE) with adequate margins, and no residual tumour was identified. On follow-up, the patient remained asymptomatic with no evidence of recurrence. The present case highlights the importance of considering DFSP in the differential diagnosis of long-standing, painless soft-tissue swellings, even at uncommon sites, and emphasises the role of histopathological evaluation and complete surgical excision in achieving optimal outcomes.