Tumour-anchored Purkinje-mediated ventricular tachycardia in a child with cardiac rhabdomyoma
Cardiac rhabdomyomas are associated with ventricular arrhythmias, but mechanisms remain uncertain. A 10-year-old boy with tuberous sclerosis complex developed verapamil-sensitive fascicular ventricular tachycardia adjacent to a residual cardiac rhabdomyoma. Electrophysiological mapping demonstrated Purkinje-mediated reentry. Catheter ablation at a tumour-adjacent site eliminated the arrhythmia, suggesting that residual rhabdomyoma may anchor a localised reentrant substrate.
Authors
- Gaku Izumi (ORCID: https://orcid.org/0000-0002-3961-0434)
- Taro Temma (ORCID: https://orcid.org/0000-0003-0480-7226)
- Daisuke Sasaki (ORCID: https://orcid.org/0000-0002-8260-0717)
Institutions
- Hokkaido University (JP)
- Sakakibara Hospital (JP)
Publication Details
- Journal
- Cardiology in the Young
- Published
- 2026-10-30
- DOI
- https://doi.org/10.1017/s1047951126124779
- Primary Topic
- Cardiac Arrhythmias and Treatments
- Type
- article
- Field-Weighted Citation Impact
- 0.00