Long-term impact of sporadic desmoid fibromatosis on work life, reproductive health, and support needs: results from the PROSa-DES study

Background Desmoid tumors (DTs; aggressive fibromatosis) are rare soft tissue tumors that predominantly affect young adults and can cause long-term morbidity. Although physical burden has been described, less is known about long-term psychosocial and functional impact. This study provides patient-reported insights into the impact of DT on employment, family planning, and psychosocial well-being. Patients and methods We analyzed data from 109 patients with DT recruited through a tertiary cancer center and a national patient advocacy group. The cohort had a median disease history of 10 years, enabling long-term assessment. Data on employment, fertility planning, and supportive care needs were collected through structured questionnaires. Results Mean age at survey was 45.7 years [standard deviation (SD) 14.1], and mean age at diagnosis was 35.8 years (SD 14.5). Nearly half of the participants had an officially recognized disability status, and ∼10% had exited the workforce. Among those employed full-time at diagnosis ( n = 49), 51% changed their career path, mainly due to reduced physical (89.9%) or psychological resilience (56.2%). Financial losses were reported by 52.2%. Among participants with incomplete family planning ( n = 59), 79.7% expressed at least moderate desire for children, yet only 17% received counseling from reproductive medicine specialists. Unmet support needs were most frequent for fear of progression (31.5%) and uncertainty about the future (35.8%). Emotional support needs decreased with longer disease duration ( P = 0.050). Conclusions DT has substantial long-term effects on employment, family planning, and psychosocial well-being. Structured survivorship approaches—including return-to-work planning, fertility counseling, and sustained psychosocial support—may help address life-course challenges in this patient population.

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Journal
ESMO rare cancers.
Published
2026-09-15
DOI
https://doi.org/10.1016/j.esmorc.2026.100526
Primary Topic
Soft tissue tumor case studies
Type
article
Field-Weighted Citation Impact
0.00

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article

Long-term impact of sporadic desmoid fibromatosis on work life, reproductive health, and support needs: results from the PROSa-DES study

Sergio Armando Zapata Bonilla, Peter Hohenberger, M.K. Schuler, R. Hoffmann et al.
ESMO rare cancers.
Soft tissue tumor case studies
article

Long-term impact of sporadic desmoid fibromatosis on work life, reproductive health, and support needs: results from the PROSa-DES study

Sergio Armando Zapata Bonilla, Peter Hohenberger, M.K. Schuler, R. Hoffmann, F. Menge, M. Eichler, C. Baumgarten
article en

Abstract

Background Desmoid tumors (DTs; aggressive fibromatosis) are rare soft tissue tumors that predominantly affect young adults and can cause long-term morbidity. Although physical burden has been described, less is known about long-term psychosocial and functional impact. This study provides patient-reported insights into the impact of DT on employment, family planning, and psychosocial well-being. Patients and methods We analyzed data from 109 patients with DT recruited through a tertiary cancer center and a national patient advocacy group. The cohort had a median disease history of 10 years, enabling long-term assessment. Data on employment, fertility planning, and supportive care needs were collected through structured questionnaires. Results Mean age at survey was 45.7 years [standard deviation (SD) 14.1], and mean age at diagnosis was 35.8 years (SD 14.5). Nearly half of the participants had an officially recognized disability status, and ∼10% had exited the workforce. Among those employed full-time at diagnosis ( n = 49), 51% changed their career path, mainly due to reduced physical (89.9%) or psychological resilience (56.2%). Financial losses were reported by 52.2%. Among participants with incomplete family planning ( n = 59), 79.7% expressed at least moderate desire for children, yet only 17% received counseling from reproductive medicine specialists. Unmet support needs were most frequent for fear of progression (31.5%) and uncertainty about the future (35.8%). Emotional support needs decreased with longer disease duration ( P = 0.050). Conclusions DT has substantial long-term effects on employment, family planning, and psychosocial well-being. Structured survivorship approaches—including return-to-work planning, fertility counseling, and sustained psychosocial support—may help address life-course challenges in this patient population.

ESMO rare cancers.Vol. 8
Johannes Gutenberg University Mainz (DE), Heidelberg University (DE), Helmholtz-Zentrum Dresden-Rossendorf (DE), University Hospital Heidelberg (DE), University Medical Center of the Johannes Gutenberg University Mainz (DE), National Center for Tumor Diseases (DE), Medical Components (United States) (US), University Medical Centre Mannheim (DE), University Hospital Carl Gustav Carus (DE)
Desmoid Tumor Research Foundation
Openalex Percentile: Top 10%
Soft tissue tumor case studies
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