Neuro-Behçet's disease: a pictorial essay.
Neuro-Behçet's disease (NBD) is a rare but serious manifestation of Behçet's disease, categorized into parenchymal and non-parenchymal forms, each with distinct clinical and imaging characteristics. Parenchymal NBD primarily af-fects the brainstem, basal ganglia, and diencephalon. On magnetic resonance imaging (MRI), acute or subacute lesions appear hyperintense on T2-weighted or fluid-attenuated inversion recovery sequences and isointense to hypointense on T1-weighted sequences, whereas chronic lesions may present as asymmetrical atrophic changes. Non-parenchy-mal NBD may present as cerebral venous thrombosis, arterial involvement, and meningeal inflammation. Here, we provide a pictorial essay on MRI central nervous system studies, mostly following an international consensus classifi-cation of NBD. Although NBD is rare, recognizing its characteristic imaging features is crucial for early diagnosis and treatment, potentially improving prognosis and reducing long-term neurological complications.
Authors
- Carlos Roberto Martins (ORCID: https://orcid.org/0000-0002-5097-8504)
- Carlos Eduardo Garcez Teixeira (ORCID: https://orcid.org/0000-0002-5340-6894)
- Ana Paula Toledo Del Rio (ORCID: https://orcid.org/0000-0002-2874-0268)
- Renan Denadai Turci (ORCID: https://orcid.org/0009-0009-3592-184X)
- Gustavo Yamada
- Fabiano Reis
- Zoraida Sachetto
Institutions
- Universidade Estadual de Campinas (UNICAMP) (BR)
Publication Details
- Journal
- PubMed
- Published
- 2026-09-12
- DOI
- https://doi.org/10.1590/0100-3984.2026.0085
- Primary Topic
- Ocular Diseases and Behçet’s Syndrome
- Type
- article
- Field-Weighted Citation Impact
- 0.00