Aortic Dissection or Aneurysm and In-Hospital Mortality in Patients With Turner Syndrome ― A Retrospective Cohort Study in Japan ―

Background: Aortic dissection and aneurysm are major causes of early mortality in Turner syndrome. However, data on aortic dissection in Turner syndrome remain limited compared with those for Marfan syndrome. We evaluated the associations of Turner syndrome and Marfan syndrome with in-hospital mortality among female patients hospitalized for aortic dissection or aneurysm, using patients without either syndrome as the common reference group for both comparisons.

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Publication Details

Journal
Circulation Journal
Published
2026-08-20
DOI
https://doi.org/10.1253/circj.cj-26-0128
Primary Topic
Genetic and Clinical Aspects of Sex Determination and Chromosomal Abnormalities
Type
article
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article

Aortic Dissection or Aneurysm and In-Hospital Mortality in Patients With Turner Syndrome ― A Retrospective Cohort Study in Japan ―

Satoko Yamaguchi, Kiyohide Fushimi, Hiroki Matsui, Akira Okada et al.
Circulation Journal
Genetic and Clinical Aspects of Sex Determination and Chromosomal Abnormalities
article

Aortic Dissection or Aneurysm and In-Hospital Mortality in Patients With Turner Syndrome ― A Retrospective Cohort Study in Japan ―

Satoko Yamaguchi, Kiyohide Fushimi, Hiroki Matsui, Akira Okada, Yuichiro Matsuo, Masaomi Nangaku, Takashi Kadowaki, Kayo Ikeda Kurakawa, Toshimasa Yamauchi, Reiko Inoue, Takafumi Inoue, Hideo Yasunaga, Masanobu Kawai
article en

Abstract

Background: Aortic dissection and aneurysm are major causes of early mortality in Turner syndrome. However, data on aortic dissection in Turner syndrome remain limited compared with those for Marfan syndrome. We evaluated the associations of Turner syndrome and Marfan syndrome with in-hospital mortality among female patients hospitalized for aortic dissection or aneurysm, using patients without either syndrome as the common reference group for both comparisons.

Circulation Journal
Saitama Prefecture (JP), Osaka Women's and Children's Hospital (JP), Individual Differences (US), Toranomon Hospital (JP), The University of Tokyo (JP)
Good health and well-being
Openalex Percentile: Top 10%
Genetic and Clinical Aspects of Sex Determination and Chromosomal Abnormalities
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Aortic Dissection or Aneurysm and In-Hospital Mortality in Patients With Turner Syndrome ― A Retrospective Cohort Study in Japan ― — Satoko Yamaguchi, Kiyohide Fushimi, et al. · Circulation Journal (2026) | TGRS Research Map | TGRS