Atypical presentations and long-term sequelae of spontaneous intracranial hypotension: illustrative cases
BACKGROUND: Spontaneous intracranial hypotension (SIH) is typically recognized by orthostatic headache and characteristic neuroimaging findings such as brain sagging and dural enhancement, but atypical manifestations and long-term sequelae remain underreported. OBSERVATIONS: The authors present 5 cases that illustrate uncommon SIH presentations and complications, including reversible cerebral vasoconstriction syndrome, sinus vein thrombosis, ventral spinal cord herniation, thoracic meningocele, secondary Arnold-Chiari malformation type I, and superficial siderosis. LESSONS: SIH may present with diverse complications beyond orthostatic headache; awareness and follow-up imaging are important for timely diagnosis and management. https://thejns.org/doi/10.3171/CASE26236.
Authors
- Johannes Goldberg (ORCID: https://orcid.org/0000-0002-6066-3549)
- Patrick Dorn (ORCID: https://orcid.org/0000-0002-7203-3122)
- Werner Josef Z'Graggen (ORCID: https://orcid.org/0000-0002-5684-4419)
- Christine Roten-Joss
- Danial Nasiri (ORCID: https://orcid.org/0009-0001-3586-2079)
- Aude Eckert
- Alexis P. R. Terrapon (ORCID: https://orcid.org/0000-0003-3721-7484)
- Eike I. Piechowiak
- Tomas Dobrocky
- Ralph T. Schär
- Katharina Lutz
- Levin Häni
- Andreas Raabe
Institutions
- University of Bern (CH)
- University Hospital of Bern (CH)
Publication Details
- Journal
- Journal of Neurosurgery Case Lessons
- Published
- 2026-08-03
- DOI
- https://doi.org/10.3171/case26236
- Primary Topic
- Neurosurgical Procedures and Complications
- Type
- article
- Field-Weighted Citation Impact
- 0.00