A hepatic enigma: Pediatric presentation of primary biliary cholangitis

Primary biliary cholangitis (PBC) is a chronic autoimmune condition characterized by destruction of intrahepatic bile ducts, leading to fibrosis and cirrhosis of the liver. It is an extremely rare pediatric disease with very few pediatric cases reported to date. Here, we report the case of a 14-year-old female who presented with elevated liver enzymes and was subsequently diagnosed with PBC. Our case raises awareness of the possibility of PBC in children.