Solitary Lesion With Features of Atrophic Papulosis in Early Childhood

Atrophic papulosis (Köhlmeier-Degos disease) is a rare thrombo-occlusive vasculopathy classically presenting with multiple porcelain-white atrophic papules and a high risk of progression to systemic involvement. We report a 2-year-old girl presenting with clinical, dermoscopic, and histologic findings of atrophic papulosis with only a solitary lesion. She had no progression of disease over the subsequent four years. This case suggests that solitary lesions of atrophic papulosis may remain clinically stable over extended follow-up.