Behçet's Disease in Idiopathic Intracranial Hypertension Without Cerebral Venous Sinus Thrombosis: Retrospective Results of a Tertiary Headache Center

In our clinic, we frequently observed the comorbidity of Behçet's disease (BD) without cerebral vein thrombosis in patients with idiopathic intracranial hypertension (IIH). This study aimed to investigate the comorbidity of isolated BD in patients with IIH. The medical records of 98 patients diagnosed with IIH were retrospectively reviewed. IIH was diagnosed by an experienced neurologist. At the diagnosis stage, patients who responded to the question "Do you have any comorbidities?" with a statement of BD had their diagnoses confirmed by a rheumatologist. The radiological images of patients diagnosed with BD were reconfirmed by a neuroradiologist, and neuro-Behçet's (NBD) disease was excluded. Isolated BD was diagnosed in 4 of 98 IIH patients (4.1%). Ninety-two of the IIH patients were female (93.9%). The mean age of the patients was 36.7±12 (18-65) years, and their mean body mass index (BMI) was 32.39 (21-49). Four BD patients were female. There was no significant difference between those with BD and those without BD regarding gender (p= 1.0). The average age of those with BD was 43.50, and the average age of those without BD was 36.41, and there was no significant difference between them (p=0.167). The mean BMI of IIH patients with BD was 35.40, while the mean BMI of IIH patients without BD was 32.26. No significant difference was found between them (p=0.323). We found a 4.1% prevalence of BD in patients with IIH. We recommend questioning IIH patients for BD symptoms in regions where BD is endemic.