Single-stage surgical repair of congenital aortopulmonary window associated with interrupted aortic arch in two toddlers: a case report

Congenital aortopulmonary window (APW) associated with interrupted aortic arch (IAA) is a rare and severe form of congenital heart disease. The optimal surgical timing and strategy remain challenging, particularly beyond infancy. We report two toddlers diagnosed with APW and IAA who underwent one-stage surgical repair. At the time of surgery, the children were 17 and 22 months old, with body weights of 6.6 kg and 8.0 kg, respectively. Both patients survived and experienced no perioperative complications. During postoperative follow-up of 12 and 19 months, respectively, the children demonstrated New York Heart Association (NYHA) class I cardiac function, with normal intracardiac anatomy and no evidence of residual shunting, vascular stenosis, or pulmonary hypertension. These cases indicate that delayed one-stage repair beyond infancy can be performed safely and effectively in selected patients with preoperative evaluation and individualized surgical planning.

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Publication Details

Journal
Journal of Cardiothoracic Surgery
Published
2026-07-17
DOI
https://doi.org/10.1186/s13019-026-04612-w
Primary Topic
Congenital Heart Disease Studies
Type
article
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article

Single-stage surgical repair of congenital aortopulmonary window associated with interrupted aortic arch in two toddlers: a case report

Mengqi Zhao, Yongqiang Jin, Junxiang Pan, Enrui Zhang et al.
Journal of Cardiothoracic Surgery
Congenital Heart Disease Studies
article

Single-stage surgical repair of congenital aortopulmonary window associated with interrupted aortic arch in two toddlers: a case report

Mengqi Zhao, Yongqiang Jin, Junxiang Pan, Enrui Zhang, Xiaoya Zhang
article en

Abstract

Congenital aortopulmonary window (APW) associated with interrupted aortic arch (IAA) is a rare and severe form of congenital heart disease. The optimal surgical timing and strategy remain challenging, particularly beyond infancy. We report two toddlers diagnosed with APW and IAA who underwent one-stage surgical repair. At the time of surgery, the children were 17 and 22 months old, with body weights of 6.6 kg and 8.0 kg, respectively. Both patients survived and experienced no perioperative complications. During postoperative follow-up of 12 and 19 months, respectively, the children demonstrated New York Heart Association (NYHA) class I cardiac function, with normal intracardiac anatomy and no evidence of residual shunting, vascular stenosis, or pulmonary hypertension. These cases indicate that delayed one-stage repair beyond infancy can be performed safely and effectively in selected patients with preoperative evaluation and individualized surgical planning.

Journal of Cardiothoracic Surgery
Beijing Hua Xin Hospital (CN)
Good health and well-being
Openalex Percentile: Top 8%
Congenital Heart Disease Studies
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Single-stage surgical repair of congenital aortopulmonary window associated with interrupted aortic arch in two toddlers: a case report — Mengqi Zhao, Yongqiang Jin, et al. · Journal of Cardiothoracic Surgery (2026) | TGRS Research Map | TGRS