Recurrent congenital pancreatic pseudocyst: an exceptionally rare case report

Abstract Background Congenital pancreatic pseudocysts are extremely rare in children, with unclear etiologyand limited reported cases. Their diagnosis is challenging, especially in true congenital cases identified before birth. Management varies based on etiology, size, and location, with surgical intervention often required. Case presentation We present a rare case of a 3-year-old girl with recurrent pancreatic pseudocyst after surgical cystectomy performed when she was8 months old. Contrast-enhanced computed tomography (CT) and endoscopic ultrasound (EUS) confirmed the diagnosis, and cystogastrostomy was performed. Fluid analysis and cytology indicated an inflamed pancreatic pseudocyst without malignancy or bacterial growth. Conclusion To our knowledge, this is the first documented case of recurrent congenital pancreatic pseudocyst following surgical correction. It highlights the need for long-term follow-up and further research on optimal management strategies for such rare cases.