Congenital Atrophic Dermatofibrosarcoma Protuberans: A Case Report and Narrative Review of the Literature
ABSTRACT Dermatofibrosarcoma protuberans is a rare dermal and subcutaneous soft‐tissue tumor, uncommon in children, characterized by CD34 positivity and COL1A1‐PDGFB fusion. Prognosis is generally good, but local recurrence risk is high, so complete excision with clear margins and six‐monthly follow‐up for three years after surgery is recommended in most cases.
Authors
- Safoura Shakoei (ORCID: https://orcid.org/0000-0001-6790-7633)
- Taha Shahbazi (ORCID: https://orcid.org/0000-0003-1529-9693)
- Sima Shamshiri Khamene (ORCID: https://orcid.org/0009-0000-1247-8472)
- Izat Mohammad Khawajah (ORCID: https://orcid.org/0009-0001-0804-7511)
Institutions
- Imam Khomeini Hospital (IR)
- Razi Hospital (IR)
- Tehran University of Medical Sciences (IR)
Publication Details
- Journal
- Clinical Case Reports
- Published
- 2026-06-25
- DOI
- https://doi.org/10.1002/ccr3.73010
- Primary Topic
- Sarcoma Diagnosis and Treatment
- Type
- article
- Field-Weighted Citation Impact
- 0.00