Multidisciplinary Dental Rehabilitation in an Adult with Noonan Syndrome: A Case Report
Noonan syndrome (NS) is a rare autosomal dominant disorder characterized by distinctive craniofacial features, congenital heart disease, bleeding disorders, and variable cognitive impairment. Oral manifestations may include malocclusion, delayed tooth eruption, enamel defects, and dental anomalies. This report describes the multidisciplinary management of a 34-year-old man with NS presenting with dental trauma, unaesthetic anterior teeth, and functional concerns. Management involved surgical extractions, endodontic treatment, and prosthetic rehabilitation, coordinated with cardiology and hematology teams to minimize systemic risks. Individualized treatment planning, behavioral adaptations, and tailored hemostatic strategies facilitated safe dental rehabilitation. This case highlights the importance of interprofessional collaboration and risk-adapted dental care in patients with complex systemic conditions.
Authors
- Carina Mehanna Zogheib (ORCID: https://orcid.org/0000-0002-0706-7262)
- Carla Zogheib (ORCID: https://orcid.org/0000-0003-0857-6998)
- Samar A Bou Jaoude
- Maha H Daou
- Nawal M El-Baba
Publication Details
- Journal
- Cureus
- Published
- 2026-06-12
- DOI
- https://doi.org/10.7759/cureus.110748
- Primary Topic
- Protein Tyrosine Phosphatases
- Type
- article
- Field-Weighted Citation Impact
- 0.00