Surgical repair of extremely late presentation of supracardiac total anomalous pulmonary vein connection: a case series

BACKGROUND: A late-presenting total anomalous pulmonary venous connection is extremely rare, and surgical repair remains a significant challenge. CASES PRESENTATION: We present two cases of surgical repair for late-presenting supracardiac total anomalous pulmonary vein connection: a 14-year-old female and a 32-year-old female. Both were successfully operated on and were discharged on postoperative days 9 and 29. The second patient had a prolonged hospital stay due to complications of acute kidney injury after surgery and the need for hemodialysis. Both patients had a small left ventricle and pulmonary hypertension preoperatively. All pulmonary veins drained to a common pulmonary vein, which drained to a left-sided vertical vein, which drained into the innominate vein. Postoperative evaluation of both patients found no pulmonary vein obstruction and good biventricular contraction. CONCLUSION: Late diagnosis may occur in TAPVC patients, but a surgical repair may still be possible.