Relative efficacy of self-managed caffeine supplementation in maintaining daily activity in a patient with ADCY5-related dyskinesia: A Case Report
Introduction: ADCY5-related dyskinesia is an autosomal dominant movement disorder with limited treatment options because many standard medications are ineffective. Caffeine has shown efficacy in ADCY5-related dyskinesia as an adenosine A2A receptor antagonist, but optimal dosing remains uncertain. Case Presentation: We report a 24-year-old woman with paroxysmal dyskinesia since early childhood, consisting of chorea, dystonia, and myoclonus upon waking. More than 15 medications failed. Whole-exome sequencing identified a mosaic ADCY5 variant (p.R418Q, 7% variant allele frequency). Caffeine escalation from 100 to 600 mg worsened symptoms. Four months later, she found that unsweetened canned coffee containing approximately 100 mg of caffeine per can, taken 1-3 times daily, reduced her symptoms and helped her maintain daily employment. In a self-controlled analysis of 39 coffee-intake events, dyskinesia episodes during the 6 h after coffee intake were significantly fewer than during the preceding 6 h (P = 0.002). Conclusion: This case demonstrates successful symptom control in ADCY5-related dyskinesia using patient-directed, low-dose caffeine therapy. The striking response suggests a narrow therapeutic window for caffeine in this condition, and that patient self-titration may be valuable in optimizing treatment response.
Authors
- Takehiko Inui (ORCID: https://orcid.org/0000-0002-7285-3817)
- Kazuhiro Haginoya (ORCID: https://orcid.org/0000-0003-0150-5716)
- Aritomo Kawashima
- Wakaba Endo
- Yukimune Okubo
- Atsuo Kikuchi (ORCID: https://orcid.org/0000-0003-1002-8739)
- Noriko Togashi (ORCID: https://orcid.org/0000-0002-4792-5460)
- Haruhiko Nakamura
- Jun Takayama
- Kaori Kodama
- Naoya Saijo
Publication Details
- Journal
- Case Reports in Neurology
- Published
- 2026-05-18
- DOI
- https://doi.org/10.1159/000552512
- Primary Topic
- Adenosine and Purinergic Signaling
- Type
- article
- Field-Weighted Citation Impact
- 0.00