Calcinosis in adult dermatomyositis: Association with anti-NXP2 antibody and a distinct anatomical distribution

Calcinosis in adult dermatomyositis is incompletely characterised. In a cohort of 191 patients, calcinosis was uncommon but strongly associated with anti-NXP2 antibodies and showed a consistent anatomical distribution affecting the thighs and buttocks. Recognition of this phenotype may aid clinical identification and future phenotypic stratification.

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Publication Details

Journal
British Journal of Dermatology
Published
2026-05-09
DOI
https://doi.org/10.1093/bjd/ljag179
Primary Topic
Inflammatory Myopathies and Dermatomyositis
Type
article
Field-Weighted Citation Impact
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article

Calcinosis in adult dermatomyositis: Association with anti-NXP2 antibody and a distinct anatomical distribution

F.S. Worsnop, Daniel Creamer, A. Connolly, Patrick Gordon et al.
British Journal of Dermatology
Inflammatory Myopathies and Dermatomyositis
article

Calcinosis in adult dermatomyositis: Association with anti-NXP2 antibody and a distinct anatomical distribution

F.S. Worsnop, Daniel Creamer, A. Connolly, Patrick Gordon, Elizabeth Wasson
article en

Abstract

Calcinosis in adult dermatomyositis is incompletely characterised. In a cohort of 191 patients, calcinosis was uncommon but strongly associated with anti-NXP2 antibodies and showed a consistent anatomical distribution affecting the thighs and buttocks. Recognition of this phenotype may aid clinical identification and future phenotypic stratification.

British Journal of Dermatology
King's College Hospital (GB)
Openalex Percentile: Top 5%
Inflammatory Myopathies and Dermatomyositis
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