Hopx(+) optic nerve head-astrocytes counter neuronal stress and glaucoma damage
Retinal ganglion cell (RGC) axons form the optic nerve (ON). Numerous age-related ON diseases, including glaucoma, the second most common cause of worldwide blindness, result from multiple RGC stressors. Nearly all ON astrocytes in the optic nerve head (ONH): the junctional region between the ON and the retina in young-adult rodents expresses the homeodomain only (Hopx) protein. Hopx(+) ONH astrocytes are depleted during aging. ONH primary cultures which include Hopx(+) astrocytes secrete extracellular vesicles (ONH-EVs) which selectively enhance RGC survival and neurite extension in culture, while extracellular vesicles (EVs) secreted from distal ON cultures lacking Hopx(+) astrocytes do not. ONH-EVs also enhance RGC survival in vivo in a rodent model of glaucoma. Combining rat ONH single-cell (scRNA-seq) sequencing with EV proteomic analysis, we identified ONH-Hopx(+) astrocyte secreted factors. We interrogated the online Broad institute scRNA-seq database for rat RGC gene expression in control animals and following rodent ON crush, an RGC stress model, to correlate ONH-astrocyte secreted factors with RGC gene expression changes. Following stress, RGCs upregulate the complementary pathways involving Hopx(+) astrocytic-associated factors, suggesting reciprocal communication. Using a highly selective transgenic Hopx-cre ONH knockdown strategy, we demonstrate that eliminating Hopx(+) astrocytes also results in upregulation of RGC stress responses. Our results implicate age-related loss of young ONH-astrocytes as a crucial factor in the development of age-related optic nerve diseases, and discuss replacing ONH associated factors as a paradigm shift for ON disease treatment.
Authors
- Zara Mehrabian
- Steven L. Bernstein (ORCID: https://orcid.org/0000-0001-7758-0136)
- Thanh Hoang (ORCID: https://orcid.org/0000-0002-7666-3842)
- Ben Mead (ORCID: https://orcid.org/0000-0001-5855-0097)
- Adam Kronk
- Jonathan A. Epstein (ORCID: https://orcid.org/0000-0001-8637-4465)
- Seth Blackshaw (ORCID: https://orcid.org/0000-0002-1338-8476)
- Stanislav I. Tomarev (ORCID: https://orcid.org/0000-0003-3042-8502)
- Esmahan Durmaz
- Yan Guo (ORCID: https://orcid.org/0009-0008-5850-8700)
- Jean Jouffroy (ORCID: https://orcid.org/0009-0001-8523-0715)
Institutions
- University of Maryland, Baltimore (US)
- Johns Hopkins University (US)
- University of Michigan (US)
- Johns Hopkins Medicine (US)
- VA Office of Research and Development (US)
- Australian College of Optometry (AU)
- Michigan Institute of Urology (US)
- National Eye Institute (US)
- University of Pennsylvania (US)
Publication Details
- Journal
- Proceedings of the National Academy of Sciences
- Published
- 2026-04-27
- DOI
- https://doi.org/10.1073/pnas.2515277123
- Primary Topic
- Neuroinflammation and Neurodegeneration Mechanisms
- Type
- article
- Field-Weighted Citation Impact
- 0.00
Funders
- National Eye Institute