Perioperative Management of a Patient with Good Syndrome and Pancytopenia Undergoing Sternotomy and Thymectomy

ABSTRACT: Good Syndrome is a rare form of immunodeficiency occurring in conjunction with thymoma. It is known to be associated with haematological manifestations, primarily pure red cell aplasia but more rarely aplastic anaemia and thrombocytopenia. We report a 61-year-old man with type AB thymoma, Good syndrome and severe pancytopenia undergoing sternotomy and thymectomy. Due to its rarity and often delayed presentation or diagnosis, case reports detailing peri-operative management are limited. This case highlights the complexity of perioperative management in Good syndrome and we detail the patient's management from initial diagnosis through major surgery and postoperative care.