Pleuroparenchymal Fibroelastosis in Connective Tissue Disease-Related Interstitial Lung Disease
: Earlier identification of PPFE in CTD-ILD is important, as misclassification may delay risk stratification and management. Longitudinal imaging, multidisciplinary evaluation, and standardized diagnostic criteria are needed to improve clinical care and guide future research.
Authors
- Cormac McCarthy (ORCID: https://orcid.org/0000-0003-2896-5210)
- Zoe Daniil (ORCID: https://orcid.org/0000-0002-1058-9125)
- George Dimeas
- E. Molloy
- Cathal Doherty
- Ilias E. Dimeas
Institutions
- University College Dublin (IE)
- University of Thessaly (GR)
- St. Vincent's University Hospital (IE)
- Development Agency of Karditsa (GR)
Publication Details
- Journal
- Journal of Clinical Medicine
- Published
- 2026-04-10
- DOI
- https://doi.org/10.3390/jcm15082886
- Primary Topic
- Interstitial Lung Diseases and Idiopathic Pulmonary Fibrosis
- Type
- article
- Field-Weighted Citation Impact
- 0.00