Bilateral Sprengel deformity with asymmetrical omovertebral connections in a child with Klippel–Feil syndrome: a rare case report

An 8-year-old male patient with bilateral Sprengel deformity, characterized by a right-sided bony omovertebral bar and a left-sided fibrous band, in the context of Klippel–Feil syndrome is presented in this case report. The patient had limited shoulder movement, a short neck, and considerable cosmetic issues. The radiological evaluation showed the omovertebral structures to be asymmetrical and a cervical fusion at C2-C3. The patient underwent 2 separate surgical procedures: the right side was operated on when the patient was 8 years old, and the left side was operated on 8 months later. The procedures involved the resection of the omovertebral structures and modified Woodward procedures for scapular repositioning. The postoperative results showed a marked improvement in shoulder abduction and cosmetic appearance with no neurovascular complications. This report emphasizes the need for early diagnosis, comprehensive imaging, and individualized surgical planning in the management of complex congenital shoulder deformities. Cite this article as: Güneş Z, Danışman M, Bekmez Ş. Bilateral Sprengel deformity with asymmetrical omovertebral connections in a child with Klippel-Feil syndrome: a rare case report. Acta Orthop Traumatol Turc., 2026; 60(2), 0313, doi: 10.5152/j.aott.2026.25313.