A Complex Case of Renal Artery Stenosis in a 3-Year-Old Patient with Neurofibromatosis Type 1 and Secondary Hypertension
We describe a case of a 3-year-old girl with neurofibromatosis type 1 presenting with arterial hypertension, in whom multimodal vascular imaging identified significant right renal artery stenosis. The patient was successfully treated with percutaneous transluminal renal angioplasty; however, post-procedural Doppler ultrasound revealed a transient vascular fistula. Changes in renal arterial inflow during the procedure may have temporarily altered pressure gradients, facilitating the opening of communication involving pre-existing compensatory collateral vessels. This case illustrates the diagnostic value of multimodal vascular imaging in pediatric hypertension and highlights a rare, self-limiting post-interventional vascular phenomenon.
Authors
- Bożena Werner (ORCID: https://orcid.org/0000-0002-6416-4106)
- Rafał Maciąg (ORCID: https://orcid.org/0000-0002-6981-565X)
- Mariusz Furmanek (ORCID: https://orcid.org/0000-0002-6713-6338)
- Piotr Skrzypczyk (ORCID: https://orcid.org/0000-0002-1959-8255)
- Jakub Pytlos (ORCID: https://orcid.org/0000-0002-9238-0391)
- Piotr Majcher (ORCID: https://orcid.org/0000-0001-6381-4421)
Institutions
- Medical University of Warsaw (PL)
Publication Details
- Journal
- Diagnostics
- Published
- 2026-03-31
- DOI
- https://doi.org/10.3390/diagnostics16071047
- Primary Topic
- Renal and Vascular Pathologies
- Type
- article
- Field-Weighted Citation Impact
- 0.00