Atypical Thrombotic Presentation of Behçet′s Disease

As Behçet′s disease (BD) is a multisystem disorder that affects blood vessels, it predisposes patients to an increased risk of thrombosis. The vessels most commonly involved are those of the lower extremities, although the dural venous system may also be affected. Deep vein thromboses (DVTs) typically occur later in the disease course and are less commonly described as an early manifestation. Herein, we present the case of a young woman who was first diagnosed with unprovoked pulmonary embolism, inferior vena cava thrombosis, and dural venous sinus thrombosis as the initial manifestations of HLA‐B51 positive BD.