Prognostic factors in interstitial lung disease-associated pulmonary hypertension: data from the HYPID cohort and the French Pulmonary Hypertension Registry

Non-invasive (6 MWD, WHO FC) and invasive (PVR) variables are associated with prognosis in patients with ILD-PH, including in patients with CPFE. PH medication might improve outcomes in this patient population.

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Publication Details

Journal
European Respiratory Journal
Published
2026-03-26
DOI
https://doi.org/10.1183/13993003.02233-2025
Primary Topic
Interstitial Lung Diseases and Idiopathic Pulmonary Fibrosis
Type
article
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article

Prognostic factors in interstitial lung disease-associated pulmonary hypertension: data from the HYPID cohort and the French Pulmonary Hypertension Registry

Athénaïs Boucly, M. F. Seronde, Thomas Lacoste-Palasset, Ana Nieves et al.
European Respiratory Journal
Interstitial Lung Diseases and Idiopathic Pulmonary Fibrosis
article

Prognostic factors in interstitial lung disease-associated pulmonary hypertension: data from the HYPID cohort and the French Pulmonary Hypertension Registry

Athénaïs Boucly, M. F. Seronde, Thomas Lacoste-Palasset, Ana Nieves, Nicolas Favrolt, Bouchra Lamia, Simon Valentin, Romain Trésorier, David Montani, Sébastien Renard, Pascal Magro, Olivier Sanchez, Élise Artaud-Macari, Marianne Riou, Rémi Diesler, Victor Valentin, Arnaud Bourdin, Aurélien Justet, Laurent Bertoletti, Fréderic Gagnadoux, the PulmoTension and OrphaLung networks, Olivier Sitbon, Martine Reynaud-Gaubert, Marc Humbert, Ari Chaouat, Céline Chabanne, Bruno Degano, Julie Traclet, Clément Boissin, Kais Ahmad, Fabien Subtil, Cécile Tromeur, Ségolène Turquier, Élise Noël-Savina, Hilario Nunes, Vincent Cottin, Nicolas Lamblin, Delphine Horeau-Langlard, Arnaud Maurac, Sébastien Quétant, François Lestelle
article en

Abstract

Non-invasive (6 MWD, WHO FC) and invasive (PVR) variables are associated with prognosis in patients with ILD-PH, including in patients with CPFE. PH medication might improve outcomes in this patient population.

European Respiratory Journal
Université Claude Bernard Lyon 1 (FR), Centre National de la Recherche Scientifique (FR), Université de Bordeaux (FR), Inserm (FR), Université de Bretagne Occidentale (FR), Université de Montpellier (FR), Université Paris Cité (FR), Aix-Marseille Université (FR), Université de Lille (FR), Université Paris-Saclay (FR), Centre Hospitalier Universitaire de Grenoble (FR), Institut Pasteur de Lille (FR), Pulmonary Hypertension Association (US), Centre Hospitalier Universitaire de Bordeaux (FR), Centre Hospitalier Universitaire de Lille (FR), Centre Hospitalier Universitaire de Nantes (FR), Centre Hospitalier Universitaire de Toulouse (FR), Mines Saint-Étienne (FR), Yale University (US), Sorbonne Université (FR), Assistance Publique Hôpitaux de Marseille (FR), Centre Hospitalier Universitaire de Besançon (FR), Institut National de Recherche pour l'Agriculture, l'Alimentation et l'Environnement (FR), Université Sorbonne Paris Nord (FR), Centre Hospitalier Universitaire de Tours (FR), Assistance Publique – Hôpitaux de Paris (FR), Center for Infection and Immunity of Lille (FR), Hospices Civils de Lyon (FR), Hôpital Européen Georges-Pompidou (FR), University of Clermont Auvergne (FR), Normandie Université (FR), Bordeaux Population Health (FR), Institut de Mathématiques de Bourgogne (FR), Hôpital Nord (FR), CHU Dijon Bourgogne (FR), Groupe Hospitalier du Havre (FR), Hôpital Pontchaillou (FR), Centre Hospitalier Universitaire de Clermont-Ferrand (FR), Hôpital Avicenne (FR), Centre Hospitalier Régional Universitaire de Brest (FR), Hôpital Louis Pradel (FR), Institute for Research and Innovation in Biomedicine (FR), Hôpital Arnaud de Villeneuve (FR), Hôpital Laennec (FR), Hôpital de la Timone (FR), Bicêtre Hospital (FR), Hôpital Civil, Strasbourg (FR), Université d'Angers (FR), Université de Rouen Normandie (FR), Université Jean Monnet (FR), Université Grenoble Alpes (FR), Université de Lorraine (FR), Université de Caen Normandie (FR)
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Openalex Percentile: Top 7%
Interstitial Lung Diseases and Idiopathic Pulmonary Fibrosis
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