An Atypical “Hot-Phase” ARVC in a PKP2 Carrier

Arrhythmogenic right ventricular cardiomyopathy (ARVC) is a leading inherited cause of sudden cardiac death in young athletes. Rarely, ARVC may present with acute myocardial injury and troponin elevation, mimicking myocarditis and delaying diagnosis.

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Publication Details

Journal
JACC Case Reports
Published
2026-03-01
DOI
https://doi.org/10.1016/j.jaccas.2026.107411
Primary Topic
Viral-associated cancers and disorders
Type
article
Field-Weighted Citation Impact
0.00
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article

An Atypical “Hot-Phase” ARVC in a PKP2 Carrier

Cedrick Mutebi, Merije Toya Chukumerije, Marius Chukwurah, Ranvir Raman Bhatia et al.
JACC Case Reports
Viral-associated cancers and disorders
article

An Atypical “Hot-Phase” ARVC in a PKP2 Carrier

Cedrick Mutebi, Merije Toya Chukumerije, Marius Chukwurah, Ranvir Raman Bhatia, Aubrey J. Grant, Oluwakorede Akele
article en

Abstract

Arrhythmogenic right ventricular cardiomyopathy (ARVC) is a leading inherited cause of sudden cardiac death in young athletes. Rarely, ARVC may present with acute myocardial injury and troponin elevation, mimicking myocarditis and delaying diagnosis.

JACC Case ReportsVol. 31(12)
Northwestern University (US), Cedars-Sinai Medical Center (US), MedStar Heart & Vascular Institute (US), UConn Health (US), University of Pennsylvania (US)
Openalex Percentile: Top 9%
Viral-associated cancers and disorders
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