Impairment of lip and tongue strength in symptomatic SMA1 patients: Results from a 4-center prospective study using the IOPI
IOPI measurements objectively demonstrate orofacial weakness in this population compared with healthy controls and may serve as a biomarker to monitor the impact of comprehensive management, including disease-modifying therapies, on oral swallowing function in SMA type 1.
Authors
- Federica Trucco (ORCID: https://orcid.org/0000-0002-1147-0126)
- Giorgia Coratti (ORCID: https://orcid.org/0000-0001-6666-5628)
- A. Vanlander
- Charlotte Colot
- Valentine Tahon
- M Pane
- Giulia Stanca
- Andrea Lizio (ORCID: https://orcid.org/0000-0002-8875-9665)
- Francesca Salmin
- Nicolas Deconinck (ORCID: https://orcid.org/0000-0003-4284-6154)
- Emilio Albamonte (ORCID: https://orcid.org/0000-0002-8465-4460)
- Sarah Muys
- Linde Van Himme
- Sansone
- Elke Everaert
- Pablo Ruiz Chicaiza
- Eugenio Mercuri
- Elke Devos
Institutions
- Università Cattolica del Sacro Cuore (IT)
- Ghent University Hospital (BE)
- Istituto Giannina Gaslini (IT)
- Agostino Gemelli University Polyclinic (IT)
- Queen Fabiola Children's University Hospital (BE)
- Centro Clinico Nemo (IT)
Publication Details
- Journal
- Journal of Neuromuscular Diseases
- Published
- 2026-03-13
- DOI
- https://doi.org/10.1177/22143602261433495
- Primary Topic
- Neurogenetic and Muscular Disorders Research
- Type
- article
- Field-Weighted Citation Impact
- 0.00