Cognitive and behavioral involvement in spinal and bulbar muscular atrophy (SBMA): a systematic review

The available evidence on cognitive and behavioral involvement in SBMA is scarce and conflicting. However, it is conceivable that at least some patients may exhibit dysexecutive-type changes, possibly reflecting a frontal system involvement.

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Publication Details

Journal
Amyotrophic Lateral Sclerosis and Frontotemporal Degeneration
Published
2026-03-13
DOI
https://doi.org/10.1080/21678421.2025.2608228
Primary Topic
Genetic Neurodegenerative Diseases
Type
article
Field-Weighted Citation Impact
0.00
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article

Cognitive and behavioral involvement in spinal and bulbar muscular atrophy (SBMA): a systematic review

Sonia Marcato, Federico Verde, Barbara Poletti, Edoardo Nicolò Aiello et al.
Amyotrophic Lateral Sclerosis and Frontotemporal Degeneration
Genetic Neurodegenerative Diseases
article

Cognitive and behavioral involvement in spinal and bulbar muscular atrophy (SBMA): a systematic review

Sonia Marcato, Federico Verde, Barbara Poletti, Edoardo Nicolò Aiello, Gianni Soraru, B. Curti, Federica Paredi, Arianna Moreschi, Giulia De Luca, Nicola Ticozzi, Vincenzo Silani
article en

Abstract

The available evidence on cognitive and behavioral involvement in SBMA is scarce and conflicting. However, it is conceivable that at least some patients may exhibit dysexecutive-type changes, possibly reflecting a frontal system involvement.

Amyotrophic Lateral Sclerosis and Frontotemporal Degeneration
University of Padua (IT), University of Milan (IT), IRCCS Istituto Auxologico Italiano (IT), Istituti di Ricovero e Cura a Carattere Scientifico (IT), Ferrari (Italy) (IT)
Openalex Percentile: Top 23%
Genetic Neurodegenerative Diseases
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