Myoepithelial carcinoma of the arm: a rare soft tissue tumor in an unusual location

Myoepithelial carcinoma (MC) is commonly identified as an aggressive tumor among the pediatric age group. Due to its rarity, it is often misidentified with other soft tissue tumors, causing a delay in management resulting in bad prognosis. A 13-year-old child presented with complaints of swelling with tenderness on his left arm above the cubital fossa involving the neurovascular bundle, diagnosed on MRI. Histopathology showed fibromuscular tissue with nests of tumor cells. He was on adjuvant therapy. However, recurrence was visualized on a follow-up scan, and he was further managed with palliative systemic chemotherapy. ME tumors can go undiagnosed, especially when they are located at an unusual site. A high index of suspicion and familiarity with the tumor’s heterogeneity can improve diagnostic accuracy.