Reversing the irreversible? A case of successful surgical repair in a late-presenting aortopulmonary window with severe pulmonary hypertension
This case suggests that operability in APW may not be irrevocably lost beyond infancy in carefully selected adolescents. It underscores the importance of individualized assessment, medical preconditioning and serial haemodynamic reassessment to unmask latent pulmonary vasoreactivity. Larger series are needed to define which late-presenting patients with APW and PH may safely benefit from definitive surgical repair.
Authors
- Aditya Agita Sembiring (ORCID: https://orcid.org/0000-0002-8854-9326)
- Rido Mulawarman (ORCID: https://orcid.org/0000-0003-2169-0971)
- Sisca Natalia Siagian (ORCID: https://orcid.org/0000-0003-1415-0387)
- Oktavia Lilyasari
- Ericko Ongko Joyo
- Muhamad Adrin Aefiansyah Putra
Institutions
- Pelita Harapan University (ID)
- University of Indonesia (ID)
- Pembuluh Darah Harapan Kita (ID)
Publication Details
- Journal
- The Egyptian Heart Journal
- Published
- 2026-03-09
- DOI
- https://doi.org/10.1186/s43044-026-00726-7
- Primary Topic
- Congenital Heart Disease Studies
- Type
- article
- Field-Weighted Citation Impact
- 0.00