Early cardiac sympathetic denervation in hereditary transthyretin amyloidosis: <sup>123</sup> I-metaiodobenzylguanidine findings and correlation with skin biopsy

Reduced l-H/M indicates early cardiac sympathetic denervation in AC, preceding clinical symptoms. Combined <sup>123</sup>I-mIBG and skin biopsy improves early detection and risk stratification in ATTRv.

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Publication Details

Journal
Amyloid
Published
2026-03-03
DOI
https://doi.org/10.1080/13506129.2026.2636657
Primary Topic
Amyloidosis: Diagnosis, Treatment, Outcomes
Type
article
Field-Weighted Citation Impact
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article

Early cardiac sympathetic denervation in hereditary transthyretin amyloidosis: 123 I-metaiodobenzylguanidine findings and correlation with skin biopsy

Andrea Truini, F Ballatore, Francesca Graziani, M. Inghilleri et al.
Amyloid
Amyloidosis: Diagnosis, Treatment, Outcomes
article

Early cardiac sympathetic denervation in hereditary transthyretin amyloidosis: 123 I-metaiodobenzylguanidine findings and correlation with skin biopsy

Andrea Truini, F Ballatore, Francesca Graziani, M. Inghilleri, Maria Silvia De Feo, Francesca Forcina, Chiara Cambieri, Maria Alfarano, Eleonora Galosi, Maria Ausilia Sciarrone, Jacopo Costantino, Giulia Marchionni, Luca Leonardi, Marco Ceccanti, M. Di Giulio, Marco Luigetti, M B Musumeci, Federica Moret, Giuseppe De Vincentis, Viviana Frantellizzi, Cristina Chimenti
article en

Abstract

Reduced l-H/M indicates early cardiac sympathetic denervation in AC, preceding clinical symptoms. Combined <sup>123</sup>I-mIBG and skin biopsy improves early detection and risk stratification in ATTRv.

Amyloid
Università Cattolica del Sacro Cuore (IT), Agostino Gemelli University Polyclinic (IT), Istituto Neurologico Mediterraneo (IT), CTO Andrea Alesini (IT), Azienda Ospedaliera Sant'Andrea (IT), Istituti di Ricovero e Cura a Carattere Scientifico (IT), Sapienza University of Rome (IT)
Openalex Percentile: Top 35%
Amyloidosis: Diagnosis, Treatment, Outcomes
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Early cardiac sympathetic denervation in hereditary transthyretin amyloidosis: <sup>123</sup> I-metaiodobenzylguanidine findings and correlation with skin biopsy — Andrea Truini, F Ballatore, et al. · Amyloid (2026) | TGRS Research Map | TGRS