Clinical and laboratory features of juvenile-onset anti-NF155 autoimmune nodopathy

Juvenile-onset NF155 AN is distinguished by motor-predominant onset, frequent tremor and characteristic electrophysiological abnormalities, yet demonstrates favourable prognosis with B-cell targeted therapy. Early recognition and timely diagnosis are essential for optimal outcomes.

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Publication Details

Journal
Journal of Neurology Neurosurgery & Psychiatry
Published
2026-03-03
DOI
https://doi.org/10.1136/jnnp-2025-337687
Primary Topic
Peripheral Neuropathies and Disorders
Type
article
Field-Weighted Citation Impact
0.00

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article

Clinical and laboratory features of juvenile-onset anti-NF155 autoimmune nodopathy

Y. Charles Lu, Cui JW, Qianwen Li, Mei‐Yan Xu et al.
Journal of Neurology Neurosurgery & Psychiatry
Peripheral Neuropathies and Disorders
article

Clinical and laboratory features of juvenile-onset anti-NF155 autoimmune nodopathy

Y. Charles Lu, Cui JW, Qianwen Li, Mei‐Yan Xu, Xinmei Wen, Zhu Wy, Yu Qian, Liang Liu, Yuwei Da, Wei Zhang, Bingchuan Xie, Hai Chen, Li Di, Yue Huang, Jianying Duo, Min Wang
article en

Abstract

Juvenile-onset NF155 AN is distinguished by motor-predominant onset, frequent tremor and characteristic electrophysiological abnormalities, yet demonstrates favourable prognosis with B-cell targeted therapy. Early recognition and timely diagnosis are essential for optimal outcomes.

Journal of Neurology Neurosurgery & Psychiatry
Hebei Medical University (CN), Shanxi Medical University (CN), Capital Medical University (CN), First Hospital of Shanxi Medical University (CN), First Affiliated Hospital of Hebei Medical University (CN)
National Natural Science Foundation of China
No poverty
Openalex Percentile: Top 42%
Peripheral Neuropathies and Disorders
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