Recurrent Paracentral Acute Middle Maculopathy Secondary to Pulmonary Arterial Hypertension: A Case Report

The definitive diagnosis of PAH requires invasive testing and is therefore frequently delayed. This case suggests that PAMM may serve as a useful ocular indicator prompting early systemic evaluation. Recognizing PAMM lesions could facilitate earlier diagnosis and intervention in patients with underlying hypoxemic conditions such as PAH.

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Publication Details

Journal
Retinal Cases & Brief Reports
Published
2026-02-25
DOI
https://doi.org/10.1097/icb.0000000000001895
Primary Topic
Retinal and Optic Conditions
Type
article
Field-Weighted Citation Impact
0.00
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article

Recurrent Paracentral Acute Middle Maculopathy Secondary to Pulmonary Arterial Hypertension: A Case Report

Taku Wakabayashi, Akira Tanikawa, Motohiro Kamei, Kotaro Tsuboi et al.
Retinal Cases & Brief Reports
Retinal and Optic Conditions
article

Recurrent Paracentral Acute Middle Maculopathy Secondary to Pulmonary Arterial Hypertension: A Case Report

Taku Wakabayashi, Akira Tanikawa, Motohiro Kamei, Kotaro Tsuboi, Akane Sobue
article en

Abstract

The definitive diagnosis of PAH requires invasive testing and is therefore frequently delayed. This case suggests that PAMM may serve as a useful ocular indicator prompting early systemic evaluation. Recognizing PAMM lesions could facilitate earlier diagnosis and intervention in patients with underlying hypoxemic conditions such as PAH.

Retinal Cases & Brief Reports
Aichi Medical University (JP), Oregon Health & Science University (US), The University of Osaka (JP)
Openalex Percentile: Top 39%
Retinal and Optic Conditions
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