The management of pregnancy for a woman with bilateral Klippel-Trenaunay syndrome: A case report

Klippel-Trenaunay syndrome is rare. It is diagnosed in childhood and the gender distribution is almost equal. A challenge arises in pregnancy, as several risks are significantly elevated, such as hemorrhage, bleeding of the varicosities, and life-threatening thromboembolic events. Due to the rarity of the condition, there is limited literature and guidelines regarding management of pregnancy for these patients. This report describes a successful pregnancy outcome in a 34-year-old primigravida with Klippel-Trenaunay syndrome. The aim is to contribute to the limited literature pertaining to this condition and emphasize the role of meticulous planning of antenatal care and birth, to help formulate clinical guidelines in the management of pregnancy in Klippel-Trenaunay syndrome. Multidisciplinary comprehensive clinical evaluation, involving obstetricians, vascular surgeons, a thrombosis team, anesthesiologists, intensivists, radiologists and intervention radiologists, along with the use of ultrasound and magnetic resonance imaging, aids in identifying the extent of disease and to individualize management.