A Systematic Review of Erdheim-Chester Disease and IgG4-Related Disease
This review provides a structured, multimodal approach to distinguish ECD from IgG4-RD, which improves diagnostic accuracy by integrating genetic testing, advanced imaging, neurological features, and treatment response. This allows clinicians to avoid misdiagnoses, implement targeted treatments, and improve patient outcomes.
Authors
- Praveen Bharath Saravanan (ORCID: https://orcid.org/0000-0002-8058-096X)
- Rithik Naik Korra
- Nikhil Kumar Balagoni
- Arvind Kunadi
- Venkata Sai Abhilash Meda
- Simhachalam Gurugubelli
Institutions
- Government Medical College (IN)
- Mercy St. Vincent Medical Center (US)
- Indiana University School of Medicine
- Indiana University – Purdue University Indianapolis (US)
- Michigan State University (US)
- Osmania Medical College (IN)
Publication Details
- Journal
- JCR Journal of Clinical Rheumatology
- Published
- 2025-11-19
- DOI
- https://doi.org/10.1097/rhu.0000000000002299
- Primary Topic
- Histiocytic Disorders and Treatments
- Type
- article
- Field-Weighted Citation Impact
- 0.00