Incidence and Survival Rates of Frontotemporal Lobar Degeneration
We observed a raw incidence rate of 0.77, thus considerably lower than in most previous reports. Incidence was substantially higher in men than in women. The prognosis from the time of diagnosis depended highly on the specific FTLD subtype. Our data are based on the large sample size and high capture rate of a central European population-based registry.
Authors
- O Neuhaus
- Dávid Brenner (ORCID: https://orcid.org/0000-0002-1535-3146)
- Elmar H. Pinkhardt (ORCID: https://orcid.org/0000-0003-1579-3472)
- Christian Dettmers (ORCID: https://orcid.org/0000-0001-9426-1559)
- Christof Kloetzsch
- Sarah M. Jesse (ORCID: https://orcid.org/0000-0002-4907-9317)
- L. Niehaus (ORCID: https://orcid.org/0000-0002-5456-0527)
- Hansjörg Bäzner (ORCID: https://orcid.org/0000-0001-8944-8239)
- Michael Ertl (ORCID: https://orcid.org/0000-0001-5271-4898)
- Christine K. Thomas
- Marko Blickhan (ORCID: https://orcid.org/0009-0003-0273-6708)
- D. Lulé
- Jens Metrikat
- Ralf Kozian
- Hubert Kimmig
- Roman Huber
- Anastasios Chatzikonstantinou (ORCID: https://orcid.org/0000-0003-0135-4807)
- Martin Hecht (ORCID: https://orcid.org/0000-0002-5168-4911)
- G. Arnold
- Dietmar Bengel
- Christian Foerch (ORCID: https://orcid.org/0000-0002-3770-7857)
- Peter Ratzka
- Deborah Wernecke (ORCID: https://orcid.org/0000-0002-6934-9257)
- Jens Volkmann (ORCID: https://orcid.org/0000-0002-9570-593X)
- Albert C. Ludolph
- Christoph Lichy
- Michael Jöbges
- Hansjörg Bäezner
- Thomas Trottenberg
- Christoph Laske
- Zeljko Uzelac
- Markus Otto
- Katharina Althaus
- Raphael Simon Peter
- Christof Kloetsch
- Matthias Buttmann
- Alfred Lindner
- Andres Frank
- Andreas Börtlein
- Jan Häckert
- James Beattie
- Frank Andres
- Klaus Demuth
- Gabriele Nagel
- Benjamin Knier
- Ingo Uttner
- Andreas Boertlein
- Dietrich Rothenbacher
- for the ALS-FTLD Registry Swabia Study Group
- Kristina Mayer-Freitag
- Christian Opherk
- Matthias Reinhard
- Markus Naumann
- Albert C. Ludolph
Institutions
- Zimmer Biomet (Netherlands) (NL)
- University of Augsburg (DE)
- Heidelberg University (DE)
- ZF Friedrichshafen (Germany) (DE)
- University Medical Center Freiburg (DE)
- German Center for Neurodegenerative Diseases (DE)
- University Hospital Augsburg (DE)
- University Hospital Heidelberg (DE)
- Kempten University of Applied Sciences (DE)
- Rems-Murr-Klinikum (DE)
- Krankenhaus vom Roten Kreuz (DE)
- Sensor-Technik Wiedemann (Germany) (DE)
- Ravensburg University of Cooperative Education (DE)
- Marienhospital Stuttgart (DE)
- Ostalb-Klinikum Aalen (DE)
- Bundeswehrkrankenhaus (DE)
- Klinikverbund Südwest (DE)
- Klinikum Esslingen (DE)
- Christophorus Kliniken (DE)
- Albstadt-Sigmaringen University (DE)
- University Children's Hospital Tübingen (DE)
- Universitätsklinikum Würzburg (DE)
- Kreiskliniken Reutlingen (DE)
- Hegau-Bodensee-Klinikum Singen (DE)
- Kliniken Schmieder (DE)
- Dermatopathologie Friedrichshafen (DE)
- Schwarzwald-Baar Klinikum (DE)
- Caritas-Krankenhaus Bad Mergentheim (DE)
- Evangelisches Diakoniekrankenhaus (DE)
- Klinikum Ludwigsburg (DE)
- Kernkraftwerk Gundremmingen (DE)
- Klinikum Kassel (DE)
- Klinikum im Friedrichshain (DE)
- University Hospital in Halle (DE)
- Diakonie-Klinikum Stuttgart (DE)
- University Hospital Ulm (DE)
- SLK-Kliniken Heilbronn (DE)
- University Medical Centre Mannheim (DE)
- Bundeswehrkrankenhaus Ulm (DE)
- Klinikum Stuttgart (DE)
- University of Tübingen (DE)
Publication Details
- Journal
- Neurology
- Published
- 2026-02-23
- DOI
- https://doi.org/10.1212/wnl.0000000000214482
- Primary Topic
- Amyotrophic Lateral Sclerosis Research
- Type
- article
- Field-Weighted Citation Impact
- 0.00