Noonan Syndrome With Multiple Lentigines Mimicking Obstructive Hypertrophic Cardiomyopathy Treated by Septal Myectomy
Septal reduction therapies may be considered in NSML with left ventricular outflow tract obstruction. Heart team discussion is essential. Surgical myectomy can provide sustained functional improvement.
Authors
- Thaís Baptista Teixeira
- Izadora Raduan Brigo (ORCID: https://orcid.org/0000-0002-8857-6498)
- Filipe Rocha da Silva
- Vagner Madrini
- Murillo Oliveira Antunes
- Ana Paula de Morais Rodrigues Barros
- Vinicius Machado Correia
- Ricardo Ribeiro Dias
- Gabrielle Batista Moreira
Institutions
- Hospital das Clínicas da Faculdade de Medicina da Universidade de São Paulo (BR)
Publication Details
- Journal
- JACC Case Reports
- Published
- 2026-02-01
- DOI
- https://doi.org/10.1016/j.jaccas.2025.106550
- Primary Topic
- Protein Tyrosine Phosphatases
- Type
- article
- Field-Weighted Citation Impact
- 0.00