Unclassified complex urogenital anomaly in a 3-year-old girl: Diagnostic and surgical challenges
Complex urogenital malformations are rare congenital anomalies that often escape existing classification systems due to marked anatomical variability. We describe a previously unreported urogenital malformation. A 3-year-old girl presented with ambiguous genitalia, a single perineal urogenital orifice, bilateral duplicated renal systems with complete vesicoureteral reflux, and vaginal agenesis. Endoscopy revealed a bladder dome diverticulum containing ureteral and cervical orifices. She underwent bilateral ureteral reimplantation and creation of an ileal neovagina with utero-neovaginal anastomosis, with an uneventful postoperative course. This anomaly represents a previously unreported entity and underscores the need for individualized, multidisciplinary management.
Authors
- Francesca Ruspi
- Michela Maffi
- M. Libri
- Ilaria Manghi
- Marcello Dòmini
- Tommaso Gargano
Institutions
- IRCCS Azienda Ospedliero-Universitaria di Bologna Policlinico di Sant'Orsola (IT)
- University of Bologna (IT)
Publication Details
- Journal
- Urology Case Reports
- Published
- 2026-02-17
- DOI
- https://doi.org/10.1016/j.eucr.2026.103379
- Primary Topic
- Ureteral procedures and complications
- Type
- article
- Field-Weighted Citation Impact
- 0.00