Unclassified complex urogenital anomaly in a 3-year-old girl: Diagnostic and surgical challenges

Complex urogenital malformations are rare congenital anomalies that often escape existing classification systems due to marked anatomical variability. We describe a previously unreported urogenital malformation. A 3-year-old girl presented with ambiguous genitalia, a single perineal urogenital orifice, bilateral duplicated renal systems with complete vesicoureteral reflux, and vaginal agenesis. Endoscopy revealed a bladder dome diverticulum containing ureteral and cervical orifices. She underwent bilateral ureteral reimplantation and creation of an ileal neovagina with utero-neovaginal anastomosis, with an uneventful postoperative course. This anomaly represents a previously unreported entity and underscores the need for individualized, multidisciplinary management.

Authors

Institutions

Publication Details

Journal
Urology Case Reports
Published
2026-02-17
DOI
https://doi.org/10.1016/j.eucr.2026.103379
Primary Topic
Ureteral procedures and complications
Type
article
Field-Weighted Citation Impact
0.00
Controls
|||
ALL TIME
JAN
FEB
MAR
APR
MAY
JUN
JUL
AUG
SEP
OCT
article

Unclassified complex urogenital anomaly in a 3-year-old girl: Diagnostic and surgical challenges

Francesca Ruspi, Michela Maffi, M. Libri, Ilaria Manghi et al.
Urology Case Reports
Ureteral procedures and complications
article

Unclassified complex urogenital anomaly in a 3-year-old girl: Diagnostic and surgical challenges

Francesca Ruspi, Michela Maffi, M. Libri, Ilaria Manghi, Marcello Dòmini, Tommaso Gargano
article en

Abstract

Complex urogenital malformations are rare congenital anomalies that often escape existing classification systems due to marked anatomical variability. We describe a previously unreported urogenital malformation. A 3-year-old girl presented with ambiguous genitalia, a single perineal urogenital orifice, bilateral duplicated renal systems with complete vesicoureteral reflux, and vaginal agenesis. Endoscopy revealed a bladder dome diverticulum containing ureteral and cervical orifices. She underwent bilateral ureteral reimplantation and creation of an ileal neovagina with utero-neovaginal anastomosis, with an uneventful postoperative course. This anomaly represents a previously unreported entity and underscores the need for individualized, multidisciplinary management.

Urology Case ReportsVol. 66
IRCCS Azienda Ospedliero-Universitaria di Bologna Policlinico di Sant'Orsola (IT), University of Bologna (IT)
Gender equality
Openalex Percentile: Top 52%
Ureteral procedures and complications
AI Navigator

Ask Laika to Summarize, Analyze, and Connect papers live on the map.

Summarize Papers & Methodologies

Extract key findings, datasets, and comparative methods across publications.

Benchmark Rankings & Visual Analytics

Rank top research institutions, authors, funders, topics, and journals by Field-Weighted Citation Impact (FWCI) and paper volume with instant charts.

Connect Distant Disciplines

Bridge topological clusters on the map to find hidden collaborative intersections.