Adult-onset Still’s disease presenting with progressive motor neuropathy
Adult-onset Still's disease should be considered in patients with fever of unknow origin and hyperferritinaemia.Neurological involvement, including polyneuropathy, may occur as an atypical manifestation.Early cytokine-targeted therapy is associated with rapid clinical improvement and better outcomes.
Authors
- Diana Moura (ORCID: https://orcid.org/0000-0002-3099-059X)
- Adriana Santos Silva
- Patrícia Fernandes
- Ana Rita Freire
- Nádia Santos
Institutions
- Instituto Politécnico de Leiria (PT)
- Administração Regional de Saúde de Lisboa e Vale do Tejo (PT)
Publication Details
- Journal
- European Journal of Case Reports in Internal Medicine
- Published
- 2026-02-16
- DOI
- https://doi.org/10.12890/2026_006231
- Primary Topic
- Autoimmune and Inflammatory Disorders Research
- Type
- article
- Field-Weighted Citation Impact
- 0.00