Adult-onset Still’s disease presenting with progressive motor neuropathy

Adult-onset Still's disease should be considered in patients with fever of unknow origin and hyperferritinaemia.Neurological involvement, including polyneuropathy, may occur as an atypical manifestation.Early cytokine-targeted therapy is associated with rapid clinical improvement and better outcomes.

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Publication Details

Journal
European Journal of Case Reports in Internal Medicine
Published
2026-02-16
DOI
https://doi.org/10.12890/2026_006231
Primary Topic
Autoimmune and Inflammatory Disorders Research
Type
article
Field-Weighted Citation Impact
0.00
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article

Adult-onset Still’s disease presenting with progressive motor neuropathy

Diana Moura, Adriana Santos Silva, Patrícia Fernandes, Ana Rita Freire et al.
European Journal of Case Reports in Internal Medicine
Autoimmune and Inflammatory Disorders Research
article

Adult-onset Still’s disease presenting with progressive motor neuropathy

Diana Moura, Adriana Santos Silva, Patrícia Fernandes, Ana Rita Freire, Nádia Santos
article en

Abstract

Adult-onset Still's disease should be considered in patients with fever of unknow origin and hyperferritinaemia.Neurological involvement, including polyneuropathy, may occur as an atypical manifestation.Early cytokine-targeted therapy is associated with rapid clinical improvement and better outcomes.

European Journal of Case Reports in Internal MedicineVol. 13(3)
Instituto Politécnico de Leiria (PT), Administração Regional de Saúde de Lisboa e Vale do Tejo (PT)
Reduced inequalities
Openalex Percentile: Top 53%
Autoimmune and Inflammatory Disorders Research
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