Clinical Features and Survival in Fibrosing Mediastinitis: A Multicenter Cohort Study
FM predominantly affects older adults and is geographically clustered in northwestern China. Smoking and elevated sPAP are key prognostic indicators for mortality. Despite substantial cardiopulmonary impairment, long-term survival remains relatively favorable.
Authors
- Yinjiang Tang
- Qixian Zeng
- Lingyan You
- Beilan Yang
- Qin Luo
- Bingyang Liu
- Jinglong Nan
- Hongyun Ruan (ORCID: https://orcid.org/0000-0003-3220-9194)
- Tao Yang
- Qunying Xi
- Yan Wu
- Yanru Liang
- Changming Xiong
- Xiaoming Zhou
- Zhihui Zhao
- Ting Wang
- Yicheng Yang
- Wenjie Yan
- Hanwen Zhang
- Yu Chen
- Gaxue Jiang
- Yinli Wang
- Xincao Tao
Institutions
- Chinese Academy of Medical Sciences & Peking Union Medical College (CN)
- Kunming Medical University (CN)
- Third People's Hospital of Chengdu (CN)
- Inner Mongolia People's Hospital (CN)
- Xuzhou Central Hospital (CN)
- Fu Wai Hospital (CN)
- First Hospital of Lanzhou University (CN)
- Lanzhou University (CN)
Publication Details
- Journal
- Respiration
- Published
- 2026-02-09
- DOI
- https://doi.org/10.1159/000550733
- Primary Topic
- IgG4-Related and Inflammatory Diseases
- Type
- article
- Field-Weighted Citation Impact
- 0.00
Funders
- Chinese Academy of Medical Sciences
- Fuwai Hospital, Chinese Academy of Medical Sciences