Inflammation and mucus properties in inherited diseases of mucociliary clearance
<title>Extract</title> Primary ciliary dyskinesia (PCD) and cystic fibrosis (CF) are inherited disorders of mucociliary clearance that lead to persistent lifelong productive cough, frequent exacerbations and, ultimately, bronchiectasis [1, 2].
Authors
- Amelia Shoemark (ORCID: https://orcid.org/0000-0001-7360-6060)
Institutions
- University of Dundee (GB)
Publication Details
- Journal
- European Respiratory Journal
- Published
- 2026-02-01
- DOI
- https://doi.org/10.1183/13993003.02426-2025
- Primary Topic
- Cystic Fibrosis Research Advances
- Type
- article
- Field-Weighted Citation Impact
- 0.00