Navigating Anatomic Complexities: Ventricular Septal Defect Closure in an Infant With Right Lung Agenesis and Extreme Dextroversion

Unilateral lung agenesis associated with congenital heart disease is very rare and the consequent malposition of the heart and mediastinal structures pose a technical challenge for definitive surgery. We describe a case of a three-month-old infant with right lung agenesis and a large ventricular septal defect who underwent successful surgical repair. The case highlights the importance of preoperative anatomic assessment and intraoperative adaption when presented with complex anatomy.