Case Report: Distinctive features of cognitive dysfunction and amelioration by antiseizure medication in neuronal intranuclear inclusion disease
NCSE can accelerate cognitive decline and ASM can improve cognitive function in NIID. Cognitive evaluation using pentagon drawing and handwriting of both morphograms and syllabograms can be useful to differentiate NIID from AD.
Authors
- Masako Kinoshita (ORCID: https://orcid.org/0000-0002-9690-3014)
- Ajay Elangovan
- Harysh Winster Suresh Babu
- Hiroya Ohara
- Masami Yamanaka
- Fumi Okada (ORCID: https://orcid.org/0009-0009-0806-5777)
- Marisse Dy Dizon
- Balachandar Vellingiri
- Mahalaxmi Iyer
- Aiko Okazaki
Institutions
- University of Santo Tomas Hospital (PH)
- University of Central Punjab (PK)
- Nara Medical University Hospital (JP)
- Osaka Minami Medical Center (JP)
- National Hospital Organization (JP)
- Utano Hospital (JP)
Publication Details
- Journal
- Frontiers in Neuroscience
- Published
- 2026-02-04
- DOI
- https://doi.org/10.3389/fnins.2026.1734078
- Primary Topic
- Genetic Neurodegenerative Diseases
- Type
- article
- Field-Weighted Citation Impact
- 0.00
Funders
- Nakatani Foundation for Advancement of Measuring Technologies in Biomedical Engineering
- Japan Society for the Promotion of Science