Case Report: Distinctive features of cognitive dysfunction and amelioration by antiseizure medication in neuronal intranuclear inclusion disease

NCSE can accelerate cognitive decline and ASM can improve cognitive function in NIID. Cognitive evaluation using pentagon drawing and handwriting of both morphograms and syllabograms can be useful to differentiate NIID from AD.

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Publication Details

Journal
Frontiers in Neuroscience
Published
2026-02-04
DOI
https://doi.org/10.3389/fnins.2026.1734078
Primary Topic
Genetic Neurodegenerative Diseases
Type
article
Field-Weighted Citation Impact
0.00

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article

Case Report: Distinctive features of cognitive dysfunction and amelioration by antiseizure medication in neuronal intranuclear inclusion disease

Masako Kinoshita, Ajay Elangovan, Harysh Winster Suresh Babu, Hiroya Ohara et al.
Frontiers in Neuroscience
Genetic Neurodegenerative Diseases
article

Case Report: Distinctive features of cognitive dysfunction and amelioration by antiseizure medication in neuronal intranuclear inclusion disease

Masako Kinoshita, Ajay Elangovan, Harysh Winster Suresh Babu, Hiroya Ohara, Masami Yamanaka, Fumi Okada, Marisse Dy Dizon, Balachandar Vellingiri, Mahalaxmi Iyer, Aiko Okazaki
article en

Abstract

NCSE can accelerate cognitive decline and ASM can improve cognitive function in NIID. Cognitive evaluation using pentagon drawing and handwriting of both morphograms and syllabograms can be useful to differentiate NIID from AD.

Frontiers in NeuroscienceVol. 20
University of Santo Tomas Hospital (PH), University of Central Punjab (PK), Nara Medical University Hospital (JP), Osaka Minami Medical Center (JP), National Hospital Organization (JP), Utano Hospital (JP)
Nakatani Foundation for Advancement of Measuring Technologies in Biomedical Engineering, Japan Society for the Promotion of Science
Openalex Percentile: Top 68%
Genetic Neurodegenerative Diseases
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Case Report: Distinctive features of cognitive dysfunction and amelioration by antiseizure medication in neuronal intranuclear inclusion disease — Masako Kinoshita, Ajay Elangovan, et al. · Frontiers in Neuroscience (2026) | TGRS Research Map | TGRS