Linear IgA bullous dermatosis in a 4-year-old child

Dear Editor, Linear IgA bullous dermatosis (LABD) is the most common autoimmune blistering disease in childhood, though it remains rare. It is characterized by tense blisters and vesicles, often in a rosette or "string of pearls" pattern, predominantly affecting non-inflamed skin. While LABD is typically self-limiting, recurrent or refractory cases pose significant therapeutic challenges. [...].

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Publication Details

Journal
Dermatology Reports
Published
2026-02-04
DOI
https://doi.org/10.4081/dr.2026.10299
Primary Topic
Autoimmune Bullous Skin Diseases
Type
article
Field-Weighted Citation Impact
0.00
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article

Linear IgA bullous dermatosis in a 4-year-old child

Giuseppe Ruggiero, Caterina Mariarosaria Giorgio, Eugenia Veronica Di Brizzi, Gaetano Licata et al.
Dermatology Reports
Autoimmune Bullous Skin Diseases
article

Linear IgA bullous dermatosis in a 4-year-old child

Giuseppe Ruggiero, Caterina Mariarosaria Giorgio, Eugenia Veronica Di Brizzi, Gaetano Licata, Filomena Barbato, Amedeo Boscaino, Giovanni Calandriello
article en

Abstract

Dear Editor, Linear IgA bullous dermatosis (LABD) is the most common autoimmune blistering disease in childhood, though it remains rare. It is characterized by tense blisters and vesicles, often in a rosette or "string of pearls" pattern, predominantly affecting non-inflamed skin. While LABD is typically self-limiting, recurrent or refractory cases pose significant therapeutic challenges. [...].

Dermatology Reports
Ospedale Sant Antonio (IT), Fatebenefratelli Hospital (IT), Santobono Children's Hospital (IT), University of Campania "Luigi Vanvitelli" (IT), Naples Anesthesia & Physician Associates (US)
Openalex Percentile: Top 68%
Autoimmune Bullous Skin Diseases
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