Surgical Management of Kartagener's Syndrome With Bronchiectasis in a Pediatric Patient: A Case Report on Right Lower Lung Lobectomy in a 9‐Year‐Old Female

Kartagner syndrome is a rare congenital autosomal recessive disorder of ciliary movement, characterized by triad of chronic sinusitis, situs inversus and bronchiectasis leading to recurrent chest and sinuses infections. The primary objectives of this case report is to highlight the presentation of this rare disorder, its surgical challenge with minimally invasive procedures, and contribute to literature of this rare syndrome in pediatric patient of 9-year-old female presented with a complaint of high grade fever and productive cough for 3 days. The X-ray findings showed Dextrocardia and right sided stomach gas, suggesting Situs inversus. The chest computerized tomography revealed right side apex beat, aortic arch on right side and right lower lobe bronchiectasis. Considering these clinical signs and radiological examination, the patient was diagnosed with Kartagener's syndrome. During Hospitalization, along with conservative treatment, the patient had undergone successful thoracoscopic right lower lobectomy for bronchiectasis secondary to Kartagener's syndrome. This case report presents a rare disorder, highlights the importance of considering Kartagener's syndrome as a differential diagnosis in patients with recurrent respiratory infection and atypical radiological findings such as situs inversus. Surgical management such as thoracoscopic right lower lung lobectomy requires expertise due to atypical anatomical arrangement. This case contributes to the existing literature of Kartagener's syndrome in pediatric patients and provides its effective comprehension of surgical management and emphasizes the need for timely intervention by experienced surgeons.