Prognostic and Functional Trajectories in Idiopathic Pulmonary Fibrosis and Systemic Autoimmune Rheumatic Disease–Associated Interstitial Lung Disease: Insights From an Italian Multicenter Cohort
SARD-ILD is associated with higher survival than IPF. Functional trajectories improved in patients with ASyS and DM, in contrast to the decline observed in those with IPF. Prognosis is more strongly influenced by the underlying diagnosis, supporting a diagnosis-centered approach to disease management.
Authors
- Cosimo Carlo De Pace (ORCID: https://orcid.org/0000-0001-9777-5598)
- Eleonora Pedretti (ORCID: https://orcid.org/0009-0007-5296-0416)
- M. Fornaro
- Pasquale Tondo (ORCID: https://orcid.org/0000-0002-1202-8567)
- Laura Bianchessi (ORCID: https://orcid.org/0000-0002-2021-0967)
- Maria Grazia Lazzaroni (ORCID: https://orcid.org/0000-0002-1860-6866)
- Paolo Airò (ORCID: https://orcid.org/0000-0001-5241-1918)
- Angelica Napoletano
- Carlo Vancheri
- G. Scioscia
- Donato Lacedonia
- Gianluca Sambataro
- Lorenzo Cavagna
- Marco Sebastiani
- Massimo Giotta
- Andreina Manfredi
- Florenzo Iannone
- Rocco Capece
- Amato A. Stabile Ianora
Institutions
- University of Foggia (IT)
- University of Modena and Reggio Emilia (IT)
- University of Parma (IT)
- Università degli Studi di Enna Kore (IT)
- University of Pavia (IT)
- University of Catania (IT)
- Azienda Socio Sanitaria Territoriale degli Spedali Civili di Brescia (IT)
- Regional Health (US)
- Policlinico Universitario di Catania (IT)
- Policlinico San Matteo Fondazione (IT)
- University of Bari Aldo Moro (IT)
- University of Brescia (IT)
Publication Details
- Journal
- The Journal of Rheumatology
- Published
- 2026-02-01
- DOI
- https://doi.org/10.3899/jrheum.2025-0610
- Primary Topic
- Inflammatory Myopathies and Dermatomyositis
- Type
- article
- Field-Weighted Citation Impact
- 0.00