Brain network pathophysiology in dystonia
Dystonia is increasingly recognized as a disorder of brain networks. This review integrates multimodal evidence from human studies to characterize the network-level pathophysiology of dystonia. Structural MRI studies using voxel-based morphometry and diffusion imaging reveal alterations in gray matter volume and white matter connectivity across the sensorimotor cortex, basal ganglia, cerebellum, and thalamus. Functional imaging modalities, including PET, fMRI, EEG, MEG, and fNIRS, demonstrate aberrant activity and connectivity in cortico-striato-pallido-thalamocortical and cerebello-thalamocortical loops. Invasive electrophysiological recordings from deep brain stimulation (DBS) provide high-resolution insights into abnormal oscillatory activity and effective connectivity within these circuits. Non-invasive brain stimulation (NIBS) techniques such as TMS, TES, and TUS provide a means of actively interrogating those networks through transient perturbation. They also provide an avenue for personalized neuromodulation. Computational models, including The Virtual Brain platform, enable integration of multimodal data to simulate dynamic network behavior. Across focal, generalized, and genetic forms of dystonia, shared patterns of network dysfunction are observed, though phenotypic and genotypic subtypes exhibit distinct topographies and circuit-level alterations. These findings underscore the importance of network dysfunction underlying dystonia. This network perspective informs the development of more targeted and individualized diagnostic and therapeutic approaches, including circuit-guided neuromodulation and closed-loop brain stimulation. Advancing multimodal and integrative methodologies will be essential to unraveling the complex dynamics underlying dystonia and translating mechanistic insights into precision interventions.
Authors
- Kristina Simonyan (ORCID: https://orcid.org/0000-0001-7444-0437)
- Joel S. Perlmutter (ORCID: https://orcid.org/0000-0003-3263-8917)
- David Peterson (ORCID: https://orcid.org/0000-0001-8151-4078)
- R. Chen
- Terrence Sanger
- Anna Sadnicka (ORCID: https://orcid.org/0000-0001-6132-2773)
- Jan K. Teller
- Philip Starr
- Myungjoo Kim
- Anthony R. McIntosh
- Andreas G. Horn
- Stephane Lehericy
- Cecile Gallea
- Emiliano Santarnecchi
- Mark Hallett
Institutions
- Brigham and Women's Hospital (US)
- Massachusetts Eye and Ear Infirmary (US)
- Centre National de la Recherche Scientifique (FR)
- Children's Hospital of Orange County (US)
- Salk Institute for Biological Studies (US)
- University Health Network (CA)
- Feinstein Institute for Medical Research (US)
- Inserm (FR)
- Simon Fraser University (CA)
- University of California, San Francisco (US)
- University of California San Diego (US)
- Sorbonne Université (FR)
- Massachusetts General Hospital (US)
- Dystonia Medical Research Foundation Canada (CA)
- Circuit Therapeutics (United States) (US)
- National Institute of Neurological Disorders and Stroke (US)
- Oxford Centre for Computational Neuroscience (GB)
- University Radiology (US)
- Institut du Cerveau (FR)
- University Hospital Cologne (DE)
- Neurological Surgery (US)
- Krembil Research Institute
- University College London (GB)
Publication Details
- Journal
- Dystonia
- Published
- 2026-01-30
- DOI
- https://doi.org/10.3389/dyst.2025.15446
- Primary Topic
- Neurological disorders and treatments
- Type
- article
- Field-Weighted Citation Impact
- 0.00