Long‐Term Outcomes and Risk Factors for Mortality After Single Ventricle Palliation for Asplenia Syndrome

Survival after single ventricle palliation for asplenia syndrome remains suboptimal, particularly when TAPVC, PA, and greater than or equal to moderate atrioventricular valve regurgitation are present in combination rather than in isolation. Improved strategies or surgical techniques are required for this complex asplenia syndrome cohort.

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Publication Details

Journal
Journal of the American Heart Association
Published
2026-01-30
DOI
https://doi.org/10.1161/jaha.125.044756
Primary Topic
Congenital Heart Disease Studies
Type
article
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article

Long‐Term Outcomes and Risk Factors for Mortality After Single Ventricle Palliation for Asplenia Syndrome

Steven J. Staffa, Shunji Sano, Shingo Kasahara, David Zurakowski et al.
Journal of the American Heart Association
Congenital Heart Disease Studies
article

Long‐Term Outcomes and Risk Factors for Mortality After Single Ventricle Palliation for Asplenia Syndrome

Steven J. Staffa, Shunji Sano, Shingo Kasahara, David Zurakowski, Yasuyuki Kobayashi, Yasuhiro Kotani, Yuhei Tokuda, Ayari Kimura
article en

Abstract

Survival after single ventricle palliation for asplenia syndrome remains suboptimal, particularly when TAPVC, PA, and greater than or equal to moderate atrioventricular valve regurgitation are present in combination rather than in isolation. Improved strategies or surgical techniques are required for this complex asplenia syndrome cohort.

Journal of the American Heart AssociationVol. 15(3)
Harvard University (US), Okayama University (JP), SHOWA Medical University Hospital (JP)
Good health and well-being
Openalex Percentile: Top 71%
Congenital Heart Disease Studies
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