The fate of the Fontan circulation
Since the first operation performed in 1968, the worldwide population of patients living with Fontan circulation is dramatically growing, with 40% reaching adulthood in the current era. Despite this remarkable improvement in survival, some patients struggle with Fontan-related complications including heart failure, arrhythmias, end-organ dysfunction, and premature death. This review aims at describing common complications of the Fontan circulation, proposing a clinical and mortality risk score to better stratify this complex population as well as exploring the current state of art in catheter interventions and transplant.
Authors
- Claudia Montanaro (ORCID: https://orcid.org/0000-0001-8613-8139)
- Raquel Prieto-Arévalo (ORCID: https://orcid.org/0000-0002-7383-8264)
- Paul Clift
- Nastasja M S de Groot
- Rosaria Barracano
- Sebastien Hascoet
Institutions
- University of Rijeka (HR)
- Queen Elizabeth Hospital Birmingham (GB)
- Erasmus MC (NL)
- Harefield Hospital (GB)
- Hospital General Universitario Gregorio Marañón (ES)
- Lung Institute (US)
- Centre Chirurgical Marie Lannelongue (FR)
- Queen Elizabeth Hospital (GB)
- Hôpital Marie Lannelongue (FR)
- Bambino Gesù Children's Hospital (IT)
- Ospedale Monaldi (IT)
- Catholic University of America (US)
- KU Leuven (BE)
Publication Details
- Journal
- European Heart Journal Supplements
- Published
- 2025-11-04
- DOI
- https://doi.org/10.1093/eurheartjsupp/suaf088
- Primary Topic
- Congenital Heart Disease Studies
- Type
- article
- Field-Weighted Citation Impact
- 0.00