Recurrent myocarditis as a clinical gateway to desmoplakin cardiomyopathy: a case report

Desmoplakin cardiomyopathy is a genetic disorder that can mimic recurrent myocarditis through inflammatory 'hot phases'. Recognition of this phenotype is essential in patients with recurrent myocarditis, especially when imaging findings show left-dominant fibrosis and arrhythmic features. Early diagnosis has important implications for treatment, prognosis, and prevention of sudden cardiac death.

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Publication Details

Journal
European Heart Journal - Case Reports
Published
2026-01-26
DOI
https://doi.org/10.1093/ehjcr/ytag062
Primary Topic
Chemotherapy-induced cardiotoxicity and mitigation
Type
article
Field-Weighted Citation Impact
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article

Recurrent myocarditis as a clinical gateway to desmoplakin cardiomyopathy: a case report

Diana Pilar Cañón, Diego A. Vargas-Hernández, Juan Francisco Figueroa, Raul Eduardo Reyes T
European Heart Journal - Case Reports
Chemotherapy-induced cardiotoxicity and mitigation
article

Recurrent myocarditis as a clinical gateway to desmoplakin cardiomyopathy: a case report

Diana Pilar Cañón, Diego A. Vargas-Hernández, Juan Francisco Figueroa, Raul Eduardo Reyes T
article en

Abstract

Desmoplakin cardiomyopathy is a genetic disorder that can mimic recurrent myocarditis through inflammatory 'hot phases'. Recognition of this phenotype is essential in patients with recurrent myocarditis, especially when imaging findings show left-dominant fibrosis and arrhythmic features. Early diagnosis has important implications for treatment, prognosis, and prevention of sudden cardiac death.

European Heart Journal - Case ReportsVol. 10(3)
Universidad El Bosque (CO), Fundación Santa Fe de Bogotá (CO)
Good health and well-being
Openalex Percentile: Top 73%
Chemotherapy-induced cardiotoxicity and mitigation
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