Clinical Characteristics and Evolution of Interstitial Lung Disease in Subtypes of Idiopathic Inflammatory Myositis With Prevalent Lung Manifestation: A Retrospective Analysis
This study highlights distinct ILD patterns across three idiopathic inflammatory myopathy subtypes, with PmPPF occurring more frequently in ASyS and anti-MDA5+ DM but not in scleromyositis. The persistence of ILD progression independent of extrapulmonary disease activity underscores the importance of ongoing pulmonary monitoring and multidisciplinary management.
Authors
- Damon Dhillon
- Jan Dutz (ORCID: https://orcid.org/0000-0003-3035-0522)
- Dora YL Chan
- Gillian Goobie
- Kun Huang
- Julia Clark
Institutions
- University of British Columbia (CA)
- University of Pittsburgh (US)
- Quest University Canada (CA)
- Surrey Memorial Hospital (CA)
- St. Paul's Hospital (CA)
- SKiN Health (CA)
- Research Canada (CA)
- St. Paul's Hospital (CA)
- Arthritis Research Centre of Canada (CA)
- BC Children's Hospital (CA)
Publication Details
- Journal
- ACR Open Rheumatology
- Published
- 2026-01-29
- DOI
- https://doi.org/10.1002/acr2.90010
- Citations
- 1
- Primary Topic
- Inflammatory Myopathies and Dermatomyositis
- Type
- article
- Field-Weighted Citation Impact
- 31.52