Fibroinflammatory Diseases of Aorta: The Inside Look

Erdheim Chester disease (ECD) is a rare fibroinflammatory disease that affects different segments of aorta. It appears as diffuse wall thickening and periaortic accumulation of scar tissue on computerized tomography (CT). The CT scans describe the size and the external structure, with minimal description of endoluminal surface of the aorta. In this report, CT images were used to visualize the interior surface of the aorta and the response to treatment in a patient with ECD.